An enzyme of the urea cycle which splits argininosuccinate to fumarate plus arginine. Its absence leads to the metabolic disease ARGININOSUCCINIC ACIDURIA in man. EC 4.3.2.1.

Synonyms: Argininosuccinase, N-(L-Argininosuccinate) arginine-lyase, Lyase, Argininosuccinate, Argininosuccinate Lyase, EC 4.3.2.1

Instance information

comment

1991; see LYASES 1975-1990 ,1991(1975); use LYASES 1975-1990

identifier

D001123

Instance relations