Congenital malformations of the central nervous system and adjacent structures related to defective neural tube closure during the first trimester of pregnancy generally occurring between days 18-29 of gestation. Ectodermal and mesodermal malformations (mainly involving the skull and vertebrae) may occur as a result of defects of neural tube closure. (From Joynt, Clinical Neurology, 1992, Ch55, pp31-41)
Synonyms: Cysts, Neuroenteric, Occult Spinal Dysraphisms, Spinal Dysraphisms, Occult, Diastematomyelia, Spinal Cord Myelodysplasias, Occult Spinal Dysraphism Sequence, Cyst, Neuroenteric, Dysraphism, Occult Spinal, Iniencephaly, Neural Tube Developmental Defects, Tethered Cord Syndromes, Acranias, Neuroenteric Cysts, Exencephaly, Craniorachischisis, Myelodysplasia, Spinal Cord, Occult Spinal Dysraphism, Neural Tube Defect, Craniorachischises, Exencephalies, Iniencephalies, Tethered Spinal Cord Syndrome, Neural Tube Defects, Dysraphisms, Occult Spinal, Defect, Neural Tube, Developmental Defects, Neural Tube, Neurenteric Cysts, Spinal Dysraphism, Occult, Acrania, Myelodysplasias, Spinal Cord, Cyst, Neurenteric, Developmental Neural Tube Defects, Neuroenteric Cyst, Spinal Cord Myelodysplasia, Neurenteric Cyst, Diastematomyelias, Cysts, Neurenteric, Defects, Neural Tube, Tethered Cord Syndrome
Instance information
do not confuse entry term SPINAL CORD MYELODYSPLASIA with MYELODYSPLASTIC SYNDROMES, a defect of bone marrow formation ,1979; for DIASTEMATOMYELIA and TETHERED CORD SYNDROME use SPINA BIFIDA OCCULTA 1991-1999; for NEURENTERIC CYST use SPINA BIFIDA OCCULTA 1991-1999, use NEURAL TUBE DEFECTS 1979-1990 ,1979; for DIASTEMATOMYELIA and TETHERED CORD SYNDROME see SPINA BIFIDA OCCULTA 1991-1999; for NEURENTERIC CYST see SPINA BIFIDA OCCULTA 1991-1999, see NEURAL TUBE DEFECTS 1979-1990
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