Group of hemorrhagic disorders in which the VON WILLEBRAND FACTOR is either quantitatively or qualitatively abnormal. They are usually inherited as an autosomal dominant trait though rare kindreds are autosomal recessive. Symptoms vary depending on severity and disease type but may include prolonged bleeding time, deficiency of factor VIII, and impaired platelet adhesion.
Synonyms: von Willebrand Disease, Angiohemophilia, von Willebrand Diseases, Disorder, Von Willebrand, Angiohemophilias, von Willebrand Disease, Recessive Form, Hemophilia, Vascular, Vascular Pseudohemophilia, von Willebrand's Diseases, Vascular Hemophilias, von Willebrand's Disease, Pseudohemophilias, Vascular, Pseudohemophilia, Vascular, Von Willebrand Disorder, Von Willebrand's Factor Deficiency, Vascular Pseudohemophilias, Vascular Hemophilia
Instance information
2010; see VON WILLEBRAND DISEASE 1999-2009; see VON WILLEBRAND'S DISEASE 1968-1998, see HEMORRHAGIC DIATHESIS 1967, see THROMBOCYTOPATHY 1963-1966 ,note specific types of Von Willebrand Disease are available ,2010(1963)
D014842