A syndrome characterized by lesions occurring on the face, scalp, or neck which consist of congenital hypoplastic malformations of cutaneous structures and which over time undergo verrucous hyperplasia. Additionally it is associated with neurological symptoms and skeletal, ophthalmological, urogenital, and cardiovascular abnormalities.

Synonyms: Feuerstein Mims Syndrome, Linear Verrucous Epidermal Nevus, Linear Sebaceous Nevus, Jadassohn Sebaceous Nevus, Nevus, Sebaceous of Jadassohn, Jadassohn Nevus Sebaceus, Inflammatory Linear Verrucose Epidermal Nevus, Syndrome, Schimmelpenning, Nevus, Verrucous Epidermal, Syndrome, Feuerstein-Mims, Nevus Phakomatoses, Organoid, Sebaceous Nevus Syndrome, Linear, Nevus Sebaceus of Jadassohn, Schimmelpenning Feuerstein Mims Syndrome, Syndrome, Schimmelpenning-Feuerstein-Mims, Sebaceous Nevus of Jadassohn, Nevus Phakomatosis, Organoid, Schimmelpenning Syndrome, Nevus Phakomatosis, Jadassohn, Verrucous Nevus, Jadassohn Nevus Phakomatosis, Phakomatoses, Organoid Nevus, Schimmelpenning-Feuerstein-Mims Syndrome, Verrucous Epidermal Nevus, Linear Sebaceous Nevus Syndrome, Phakomatosis, Jadassohn Nevus, Feuerstein-Mims Syndrome, Nevus, Linear Sebaceous, Organoid Nevus Phakomatoses, Nevus, Verrucous, Sebaceous Nevus, Linear, Organoid Nevus Phakomatosis, Epidermal Nevus, Verrucous, Phakomatosis, Organoid Nevus, Inflammatory Linear Verrucous Epidermal Naevus

Instance information

comment

2010 (2008) ,2010; see NEVUS SEBACEOUS OF JADASSOHN 2008-2009

identifier

D054000