A family of mesenchymal tumors composed of histologically and immunohistochemically distinctive perivascular epithelioid cells. These cells do not have a normal anatomic homolog. (From Fletcher CDM, et. al., World Health Organization Classification of Tumors: Pathology and Genetics of Tumors of Soft Tissue and Bone, 2002).

PEComas of the falciform ligament / ligamentum teres.

PEComas containing glycogen-rich clear cytoplasm and found in the lung and a wide range of extrapulmonary sites.

Synonyms: Myomelanocytic Tumors, Clear-Cell, Perivascular Epithelioid Cell Tumor, PEComa, Perivascular Epithelioid Cell Neoplasms, Clear Cell Myomelanocytic Tumors, Tumor, Clear-Cell Myomelanocytic, Clear Cell Sugar Tumors, PEComas, Clear Cell Sugar Tumor, Clear-Cell Myomelanocytic Tumors, Neoplasms, Perivascular Epithelioid Cell, Perivascular Epithelioid Cell Neoplasm, Clear-Cell Sugar Tumor, Clear-Cell Myomelanocytic Tumor, Tumors, Clear-Cell Myomelanocytic, Sugar Tumor, Clear-Cell, Perivascular Epithelioid Cell Tumors, Clear-Cell Sugar Tumors, Tumor, Clear-Cell Sugar, Myomelanocytic Tumor, Clear-Cell, Tumors, Clear-Cell Sugar, CCMMT, Sugar Tumors, Clear-Cell, Clear Cell Myomelanocytic Tumor