A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change.

Synonyms: Pulmonary Fibrosis, Idiopathic, Fibrocystic Pulmonary Dysplasias, Fibrosing Alveolitides, Cryptogenic, Pneumonitides, Usual Interstitial, Pulmonary Dysplasia, Fibrocystic, Idiopathic Pulmonary Fibrosis, Pulmonary Fibroses, Idiopathic, Cryptogenic Fibrosing Alveolitides, Fibrocystic Pulmonary Dysplasia, Pneumonitis, Usual Interstitial, Idiopathic Pulmonary Fibrosis, Familial, Usual Interstitial Pneumonitides, Dysplasia, Fibrocystic Pulmonary, Fibrosing Alveolitis, Cryptogenic, Idiopathic Pulmonary Fibroses, Familial Idiopathic Pulmonary Fibrosis, Usual Interstitial Pneumonias, Idiopathic Fibrosing Alveolitis, Chronic Form, Interstitial Pneumonitis, Usual, Interstitial Pneumonia, Usual, Usual Interstitial Pneumonia, Cryptogenic Fibrosing Alveolitis, Usual Interstitial Pneumonitis